{"id":10141,"date":"2024-04-01T16:16:39","date_gmt":"2024-04-01T14:16:39","guid":{"rendered":"https:\/\/www.afaf.asso.fr\/?page_id=10141"},"modified":"2024-04-01T17:13:39","modified_gmt":"2024-04-01T15:13:39","slug":"veille-bibliographique-recherche","status":"publish","type":"page","link":"https:\/\/www.afaf.asso.fr\/la-recherche\/veille-bibliographique-recherche\/","title":{"rendered":"Veille bibliographique"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"10141\" class=\"elementor elementor-10141\" data-elementor-post-type=\"page\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-6338cd8 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"6338cd8\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-4678a0c\" data-id=\"4678a0c\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ee40a8b elementor-widget elementor-widget-text-editor\" data-id=\"ee40a8b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Cette page propose une veille bibliographique <span style=\"text-decoration: underline;\">non exhaustive<\/span> de la litt\u00e9rature scientifique en rapport avec l\u2019Ataxie de Friedreich, comprenant une s\u00e9lection&nbsp; d\u2019articles class\u00e9s par th\u00e9matique. Vous trouverez le titre traduit de l\u2019article, ainsi que le lien d\u2019acc\u00e8s \u00e0 la publication, et parfois un court commentaire de l\u2019article.<br>Nous vous proposons d\u2019interagir avec les membres du groupe recherche de l\u2019AFAF pour toute question concernant les articles mentionn\u00e9s (traductions, explications), pour \u00e9changer tout simplement, ou pour enrichir cette section. Merci d\u2019\u00e9crire \u00e0 <a href=\"mailto:recherche@afaf.asso.fr\">recherche@afaf.asso.fr<\/a> pour toute question ou suggestion.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-00465c3 lien-ancre elementor-widget elementor-widget-text-editor\" data-id=\"00465c3\" data-element_type=\"widget\" data-e-type=\"widget\" id=\"sommaire_biblio\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tSommaire :\n<ul>\n \t<li><a href=\"#revue_generale\">Revue g\u00e9n\u00e9rale de la litt\u00e9rature<\/a><\/li>\n \t<li><a href=\"#therapeutiques\">Th\u00e9rapeutiques (par ordre alphab\u00e9tique)<\/a><\/li>\n \t<li><a href=\"#organes\">Par organes ou sympt\u00f4mes<\/a><\/li>\n \t<li><a href=\"#biologie\">Biologie fondamentale<\/a><\/li>\n \t<li><a href=\"#exam_paracliniques\">Examens paracliniques<\/a><\/li>\n<\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-e480cea elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e480cea\" data-element_type=\"section\" data-e-type=\"section\" id=\"revue_generaka\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-4961bd7\" data-id=\"4961bd7\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-8f2e759 elementor-widget elementor-widget-heading\" data-id=\"8f2e759\" data-element_type=\"widget\" data-e-type=\"widget\" id=\"sommaire_biblio\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Revue g\u00e9n\u00e9rale de la litt\u00e9rature<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-8a66026 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"8a66026\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-inner-section elementor-element elementor-element-839f2fc elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"839f2fc\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-custom\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-78fdb81\" data-id=\"78fdb81\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-0a33844 elementor-widget elementor-widget-text-editor\" data-id=\"0a33844\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Ataxies h\u00e9r\u00e9ditaires r\u00e9cessives &#8211; c\u00e9r\u00e9belleuses et aff\u00e9rentes &#8211; d\u00e9fis cliniques et orientations futures <\/strong>(2022)<ul><li>R\u00e9ferences :\u00a0 Beaudin M, Manto M, Schmahmann JD, Pandolfo M, Dupre N. <em>Nat Rev Neurol.<\/em> 2022 May;18(5):257-272.<\/li><li>Article : <a href=\"https:\/\/www.nature.com\/articles\/s41582-022-00634-9\" target=\"_blank\" rel=\"noopener\">Recessive cerebellar and afferent ataxias \u2014 clinical challenges and future directions | Nature Reviews Neurology<\/a><\/li><li><em>Remarque de lecture AFAF<\/em> : Dans cette revue de la litt\u00e9rature, les auteurs \u00e9voquent les \u00e9tiologies et perspectives th\u00e9rapeutiques des ataxies r\u00e9cessives, dont principalement l\u2019ataxie de Friedreich. Ils rapportent les diff\u00e9rentes approches th\u00e9rapeutiques pour l\u2019AF : l\u2019augmentation de la transcription du g\u00e8ne FXN pour produire plus de frataxine, le remplacement direct de la prot\u00e9ine ou l\u2019augmentation de l\u2019expression du frataxine, la r\u00e9duction du stress oxydatif. Les auteurs s\u2019interrogent sur les difficult\u00e9s rencontr\u00e9es par de nombreux essais cliniques prometteurs, qui n\u2019aboutissent pas ensuite. Ils soulignent l\u2019importance de la conception efficace des essais cliniques : identifier la population de patients dans laquelle la progression de la maladie peut le mieux \u00eatre d\u00e9tecter et s\u00e9lectionnes les mesures de r\u00e9sultats les plus sensibles et les plus robustes.<\/li><\/ul><\/li><li><strong>Ataxie de Friedreich: \u00e9tat actuel des connaissances et perspectives d\u2019avenir des th\u00e9rapies ax\u00e9es sur les mitochondries<\/strong> (2021)<ul><li>R\u00e9f\u00e9rences : Pallard\u00f3 FV, Pagano G, Rodr\u00edguez LR, Gonzalez-Cabo P, Lyakhovich A, Trifuoggi M. <em>Transl Res<\/em>. 2021 Mar;229:135-141.<\/li><li><a href=\"https:\/\/www.translationalres.com\/article\/S1931-5244(20)30204-8\/fulltext\" target=\"_blank\" rel=\"noopener\">Article : Friedreich Ataxia: current state-of-the-art, and future prospects for mitochondrial-focused therapies &#8211; Translational Research<\/a><\/li><\/ul><\/li><li><strong>Recommandations pour la prise en charge de l\u2019Ataxie de Friedreich: bonnes pratiques dans les maladies rares<\/strong> (2022)<ul><li>R\u00e9f\u00e9rences : Corben LA, Collins V, Milne S, Farmer J, Musheno A, Lynch D, Subramony S, Pandolfo M, Schulz JB, Lin K, Delatycki MB; Clinical Management Guidelines Writing Group. <em>Orphanet J Rare Dis.<\/em> 2022 Nov 12;17(1):415.<\/li><li><a href=\"https:\/\/ojrd.biomedcentral.com\/articles\/10.1186\/s13023-022-02568-3\" target=\"_blank\" rel=\"noopener\">Article : Clinical management guidelines for Friedreich ataxia: best practice in rare diseases | Orphanet Journal of Rare Diseases | Full Text (biomedcentral.com)<\/a><\/li><\/ul><\/li><li><strong>Ataxie de Friedreich: caract\u00e9ristiques cliniques et nouveaux d\u00e9veloppements<\/strong> (2022)<ul><li>R\u00e9f\u00e9rences : Keita M, McIntyre K, Rodden LN, Schadt K, Lynch DR. Friedreich ataxia: clinical features and new developments. <em>Neurodegener Dis Manag<\/em>. 2022 Oct;12(5):267-283.<\/li><li>Article : <a href=\"https:\/\/www.futuremedicine.com\/doi\/10.2217\/nmt-2022-0011\" target=\"_blank\" rel=\"noopener\">Friedreich ataxia: clinical features and new developments | Neurodegenerative Disease Management (futuremedicine.com)<\/a><\/li><\/ul><\/li><li><strong>Repositionnement m\u00e9dicamenteux dans l\u2019ataxie de Friedreich<\/strong> (2022)<ul><li>R\u00e9f\u00e9rences : Rufini A, Malisan F, Cond\u00f2 I, Testi R.. <em>Front Neurosci.<\/em> 2022 Feb;16:814445.<\/li><li>Article : <a href=\"https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2022.814445\/full\" target=\"_blank\" rel=\"noopener\">Frontiers | Drug Repositioning in Friedreich Ataxia (frontiersin.org)<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-dd61f9b\" data-id=\"dd61f9b\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-be0c783 elementor-widget elementor-widget-text-editor\" data-id=\"be0c783\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Documents associ\u00e9s<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-8009525 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"8009525\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-aa427f4 pdf2-colonne-laterale nouvelle-fenetre elementor-widget elementor-widget-text-editor\" data-id=\"aa427f4\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Retrouver la version PDF de la biographique propos\u00e9e ici<\/p><ul><li><a href=\"https:\/\/www.afaf.asso.fr\/wp-content\/uploads\/2023\/07\/AFAF-groupe-recherche-Revue-de-la-litterature-AF-juillet-2023.pdf\">AFAF groupe recherche &#8211; revue de la litt\u00e9rature d&#8217;articles scientifiques<\/a> &#8211; juillet 2023<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-62c1e2f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"62c1e2f\" data-element_type=\"section\" data-e-type=\"section\" id=\"therapeutiques\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-e9fed7b\" data-id=\"e9fed7b\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-05a2799 elementor-widget elementor-widget-heading\" data-id=\"05a2799\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Th\u00e9rapeutiques (par ordre alphab\u00e9tique)<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-45a5ca1 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"45a5ca1\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-inner-section elementor-element elementor-element-f743dc8 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f743dc8\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-custom\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-13cfc42\" data-id=\"13cfc42\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ffd11a5 elementor-widget elementor-widget-heading\" data-id=\"ffd11a5\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Dimethyl-fumarate<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-cb5c1c7 elementor-widget elementor-widget-text-editor\" data-id=\"cb5c1c7\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Le Dimethyl fumarate augmente l\u2019expression de la frataxine: une th\u00e9rapeutique potentielle pour l\u2019ataxie de Friedreich <\/strong>(2019)<strong><br \/><\/strong><ul><li>R\u00e9ferences : Jasoliya M, Sacca F, Sahdeo S, Chedin F, Pane C, Brescia Morra V, Filla A, Pook M, Cortopassi G. <em>PLoS One<\/em>. 2019 Jun 3;14(6):e0217776.<\/li><li>Article : <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC6546270\/\" target=\"_blank\" rel=\"noopener\">Dimethyl fumarate dosing in humans increases frataxin expression: A potential therapy for Friedreich\u2019s Ataxia &#8211; PMC (nih.gov)<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-e94a266 elementor-widget elementor-widget-text-editor\" data-id=\"e94a266\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Le Dimethyl fumarate augmente l\u2019expression de la frataxine: une th\u00e9rapeutique potentielle pour l\u2019ataxie de Friedreich <\/strong>(2019)<strong><br \/><\/strong><ul><li>R\u00e9ferences : Jasoliya M, Sacca F, Sahdeo S, Chedin F, Pane C, Brescia Morra V, Filla A, Pook M, Cortopassi G. <em>PLoS One<\/em>. 2019 Jun 3;14(6):e0217776.<\/li><li>Article : <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC6546270\/\" target=\"_blank\" rel=\"noopener\">Dimethyl fumarate dosing in humans increases frataxin expression: A potential therapy for Friedreich\u2019s Ataxia &#8211; PMC (nih.gov)<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-d010dcd elementor-widget elementor-widget-heading\" data-id=\"d010dcd\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Etravirine<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-11b9399 elementor-widget elementor-widget-text-editor\" data-id=\"11b9399\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Le repositionnement m\u00e9dicamenteux identifie l\u2019etravirine comme une th\u00e9rapeutique potentielle dans l\u2019ataxie de Friedreich<\/strong> (2019)<ul><li>R\u00e9ferences : Alfedi G, Luffarelli R, Cond\u00f2 I, Pedini G, Mannucci L, Massaro DS, Benini M, Toschi N, Alaimo G, Panarello L, Pacini L, Fortuni S, Serio D, Malisan F, Testi R, Rufini A. <em>Mov Disord<\/em>. 2019 Mar;34(3):323-334.<\/li><li>Article : <a href=\"https:\/\/movementdisorders.onlinelibrary.wiley.com\/doi\/10.1002\/mds.27604\" target=\"_blank\" rel=\"noopener\">Drug repositioning screening identifies etravirine as a potential therapeutic for friedreich&#8217;s ataxia &#8211; Alfedi &#8211; 2019 &#8211; Movement Disorders &#8211; Wiley Online Library<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-b634772 elementor-widget elementor-widget-heading\" data-id=\"b634772\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Exenatide<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-aeb5c94 elementor-widget elementor-widget-text-editor\" data-id=\"aeb5c94\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul>\n \t<li><strong>L\u2019exenatide induit l\u2019expression de la frataxine et am\u00e9liore la fonction mitochondriale dans l\u2019ataxie de Freidreich<\/strong> (2019)\n<ul>\n \t<li>R\u00e9ferences : Mariana Igoillo-Esteve, Ana F Oliveira, Cristina Cosentino, Federica Fantuzzi, C\u00e9line Demarez, Sanna Toivonen, Am\u00e9lie Hu, Satyan Chintawar, Miguel Lopes, Nathalie Pachera, Ying Cai, Baroj Abdulkarim, Myriam Rai, Lorella Marselli, Piero Marchetti, Mohammad Tariq, Jean-Christophe Jonas, Marina Boscolo, Massimo Pandolfo, D\u00e9cio L Eizirik, Miriam Cnop. <em>JCI Insight.<\/em>2020;5(2):e134221<\/li>\n \t<li>Article : <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/31877117\/\" target=\"_blank\" rel=\"noopener\">Exenatide induces frataxin expression and improves mitochondrial function in Freidriech ataxia\u00a0<\/a><\/li>\n<\/ul>\n<\/li>\n<\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-c665964 elementor-widget elementor-widget-heading\" data-id=\"c665964\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Idebenone<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-c293646 elementor-widget elementor-widget-text-editor\" data-id=\"c293646\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Etude de Phase 3, en double aveugle, contr\u00f4l\u00e9e contre placebo, de l\u2019utilisation de l\u2019Id\u00e9b\u00e9none dans l\u2019ataxie de Friedreich<\/strong> (2010)<br \/><ul><li>Lynch DR, Perlman SL, Meier T. <em>Arch Neurol<\/em>. 2010 Aug;67(8):941-7.<\/li><li>Article : <a href=\"https:\/\/jamanetwork.com\/journals\/jamaneurology\/fullarticle\/800798\" target=\"_blank\" rel=\"noopener\">A Phase 3, Double-blind, Placebo-Controlled Trial of Idebenone in Friedreich Ataxia | Genetics and Genomics | JAMA Neurology | JAMA Network<\/a><\/li><\/ul><\/li><li><strong>Effets neurologiques de doses \u00e9lev\u00e9es d\u2019idebenone dans l\u2019ataxie de friedreich : un essai randomis\u00e9, contr\u00f4l\u00e9 contre placebo.<\/strong> (2007)<br \/><ul><li>Di Prospero NA, Baker A, Jeffries N, Fischbeck KH. Lancet Neurol. 2007 Oct;6(10):878-86. <\/li><li>Article : <a href=\"https:\/\/www.thelancet.com\/journals\/laneur\/article\/PIIS1474-4422(07)70220-X\/fulltext\" target=\"_blank\" rel=\"noopener\">Neurological effects of high-dose idebenone in patients with Friedreich&#8217;s ataxia: a randomised, placebo-controlled trial &#8211; The Lancet Neurology<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-5bd2302 elementor-widget elementor-widget-heading\" data-id=\"5bd2302\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Nicotinamide<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-cc28c07 elementor-widget elementor-widget-text-editor\" data-id=\"cc28c07\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Effets \u00e9pig\u00e9n\u00e9tiques et neurologiques et s\u00e9curit\u00e9 de doses importantes de nicotinamide dans l\u2019ataxie de Friedreich : une \u00e9tude exploratoire, ouverte, en augmentation de doses <\/strong> (2014)<ul><li>Libri V, Yandim C, Athanasopoulos S, Loyse N, Natisvili T, Law PP, Chan PK, Mohammad T, Mauri M, Tam KT, Leiper J, Piper S, Ramesh A, Parkinson MH, Huson L, Giunti P, Festenstein R. <em>Lancet<\/em>. 2014 Aug 9;384(9942):504-13.<\/li><li>Article : <a href=\"https:\/\/www.thelancet.com\/journals\/lancet\/article\/PIIS0140-6736(14)60382-2\/fulltext\" target=\"_blank\" rel=\"noopener\">Epigenetic and neurological effects and safety of high-dose nicotinamide in patients with Friedreich&#8217;s ataxia: an exploratory, open-label, dose-escalation study &#8211; The Lancet<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-5e8d59b elementor-widget elementor-widget-heading\" data-id=\"5e8d59b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Nomlabofusp<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-5b4062d elementor-widget elementor-widget-text-editor\" data-id=\"5b4062d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><p><strong>S\u00e9curit\u00e9, pharmacocin\u00e9tique et pharmacodynamie du nomlabofusp (CTI-1601) dans l\u2019ataxie de Friedreich <\/strong>(2024)<\/p><ul><li><p>Clayton R, Galas T, Scherer N, Farmer J, Ruiz N, Hamdani M, Schecter D, Bettoun D. <em>Ann Clin Transl Neurol<\/em>. 2024 Feb 4.<\/p><\/li><li>Article :<p><a href=\"https:\/\/onlinelibrary.wiley.com\/doi\/full\/10.1002\/acn3.51971\" target=\"_blank\" rel=\"noopener\">Safety, pharmacokinetics, and pharmacodynamics of nomlabofusp (CTI\u20101601) in Friedreich&#8217;s ataxia &#8211; Clayton &#8211; Annals of Clinical and Translational Neurology &#8211; Wiley Online Library<\/a><\/p><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-dbfb1c3 elementor-widget elementor-widget-heading\" data-id=\"dbfb1c3\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Omaveloxolone<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-0e53258 elementor-widget elementor-widget-text-editor\" data-id=\"0e53258\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul>\n \t<li><strong>Efficacit\u00e9 de l\u2019omaveloxolone dans l\u2019ataxie de Friedreich: une analyse de d\u00e9but diff\u00e9r\u00e9 de l\u2019extension de MOXIe <\/strong> (2023)\n<ul>\n \t<li>Lynch DR, Chin MP, Boesch S, Delatycki MB, Giunti P, Goldsberry A, Hoyle JC, Mariotti C, Mathews KD, Nachbauer W, O&#8217;Grady M, Perlman S, Subramony SH, Wilmot G, Zesiewicz T, Meyer CJ. <em>Mov Disord<\/em>. 2023 Feb;38(2):313-320.<\/li>\n \t<li>Article : <a href=\"https:\/\/movementdisorders.onlinelibrary.wiley.com\/doi\/10.1002\/mds.29286\" target=\"_blank\" rel=\"noopener\">Efficacy of Omaveloxolone in Friedreich&#8217;s Ataxia: Delayed\u2010Start Analysis of the MOXIe Extension &#8211; Lynch &#8211; 2023 &#8211; Movement Disorders &#8211; Wiley Online Library<\/a><\/li>\n<\/ul>\n<\/li>\n \t<li><strong>S\u00e9curit\u00e9 et efficacit\u00e9 de l\u2019omaveloxolone dans l\u2019ataxie de Friedreich<\/strong> (2021)\n<ul>\n \t<li>Lynch DR, Chin MP, Delatycki MB, Subramony SH, Corti M, Hoyle JC, Boesch S, Nachbauer W, Mariotti C, Mathews KD, Giunti P, Wilmot G, Zesiewicz T, Perlman S, Goldsberry A, O&#8217;Grady M, Meyer CJ. <em>Ann Neurol<\/em>. 2021 Feb;89(2):212-225.<\/li>\n \t<li>Article : <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC7894504\/\" target=\"_blank\" rel=\"noopener\">Safety and Efficacy of Omaveloxolone in Friedreich Ataxia (MOXIe Study) &#8211; PMC (nih.gov)<\/a><\/li>\n<\/ul>\n \t<li><strong>Comparaison par score de propension du traitement \u00e0 l&#8217;omaveloxolone avec les donn\u00e9es de l&#8217;histoire naturelle de l&#8217;ataxie de Friedreich <\/strong>(2024) \n<ul>\n<li>Lynch DR, Goldsberry A, Rummey C, Farmer J, Boesch S, Delatycki MB, Giunti P, Hoyle JC, Mariotti C, Mathews KD, Nachbauer W, Perlman S, Subramony SH, Wilmot G, Zesiewicz T, Weissfeld L, Meyer C. <em>Ann Clin Transl Neurol.<\/em> 2024 Jan;11(1):4-16.<\/li>\n<li> Article : <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/37691319\/\" target=\"_blank\" rel=\"noopener\">Propensity matched comparison of omaveloxolone treatment to Friedreich ataxia natural history data &#8211; PubMed (nih.gov)<\/a><\/li>\n<\/ul>\n<\/li>\n<\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-0dc3ef3 elementor-widget elementor-widget-heading\" data-id=\"0dc3ef3\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Thiamine<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-34aa635 elementor-widget elementor-widget-text-editor\" data-id=\"34aa635\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Traitement au long cours par thiamine comme th\u00e9rapeutique envisageable dans l\u2019ataxie de Friedreich<\/strong> (2016)<ul><li>Costantini A, Laureti T, Pala MI, Colangeli M, Cavalieri S, Pozzi E, Brusco A, Salvarani S, Serrati C, Fancellu R. <em>J Neurol<\/em>. 2016 Nov;263(11):2170-2178.<\/li><li>Article : <a href=\"https:\/\/iris.unito.it\/handle\/2318\/1627405\" target=\"_blank\" rel=\"noopener\">Long-term treatment with thiamine as possible medical therapy for Friedreich ataxia (unito.it)<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-20df6cd elementor-widget elementor-widget-heading\" data-id=\"20df6cd\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Vatiquinone (PTC-743)<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-028ccf2 elementor-widget elementor-widget-text-editor\" data-id=\"028ccf2\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Essai contr\u00f4l\u00e9, randomis\u00e9, en double aveugle, \u00e9tauduant l\u2019EPI-743 dans l\u2019ataxie de fridreich.<\/strong> (2018)<ul><li>Zesiewicz T, Salemi JL, Perlman S, Sullivan KL, Shaw JD, Huang Y, Isaacs C, Gooch C, Lynch DR, Klein MB. <em>Neurodegener Dis Manag.<\/em> 2018 Aug;8(4):233-242.<\/li><li>Article : <a href=\"https:\/\/www.futuremedicine.com\/doi\/10.2217\/nmt-2018-0013?url_ver=Z39.88-2003&amp;rfr_id=ori%3Arid%3Acrossref.org&amp;rfr_dat=cr_pub++0pubmed\" target=\"_blank\" rel=\"noopener\">Double-blind, randomized and controlled trial of EPI-743 in Friedreich&#8217;s ataxia | Neurodegenerative Disease Management (futuremedicine.com)<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-30c1726\" data-id=\"30c1726\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7521819 elementor-widget elementor-widget-text-editor\" data-id=\"7521819\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Documents associ\u00e9s<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-ea881a5 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"ea881a5\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-8a00adc pdf2-colonne-laterale nouvelle-fenetre elementor-widget elementor-widget-text-editor\" data-id=\"8a00adc\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Retrouver la version PDF de la biographique propos\u00e9e ici<\/p><ul><li><a href=\"https:\/\/www.afaf.asso.fr\/wp-content\/uploads\/2023\/07\/AFAF-groupe-recherche-Revue-de-la-litterature-AF-juillet-2023.pdf\">AFAF groupe recherche &#8211; revue de la litt\u00e9rature d&#8217;articles scientifiques<\/a> &#8211; juillet 2023<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-60a02b5 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"60a02b5\" data-element_type=\"section\" data-e-type=\"section\" id=\"organes\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-298547a\" data-id=\"298547a\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-69cb43b elementor-widget elementor-widget-heading\" data-id=\"69cb43b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Par organes ou sympt\u00f4mes<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-1378316 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"1378316\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-inner-section elementor-element elementor-element-c54dfdf elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"c54dfdf\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-custom\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-87f9ded\" data-id=\"87f9ded\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-770ed96 elementor-widget elementor-widget-heading\" data-id=\"770ed96\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Coeur <\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-24719b3 elementor-widget elementor-widget-text-editor\" data-id=\"24719b3\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>La recherche cardiovasculaire dans l\u2019ataxie de Friedreich : dissensions entre besoins et opportunit\u00e9s<\/strong> (2022)<ul><li>Payne RM. JACC <em>Basic Transl Sci.<\/em> 2022 Jul 13;7(12):1267-1283.<\/li><li>Article : <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC9831864\/\" target=\"_blank\" rel=\"noopener\">Cardiovascular Research in Friedreich Ataxia &#8211; PMC (nih.gov)<\/a><\/li><\/ul><\/li><li><strong>Suivi sur 22 ans du devenir cardiaque \u00e0 long terme et facteurs pr\u00e9dictifs de survie dans l\u2019ataxie de Friedreich<\/strong> (2015)<ul><li>Pousset F, Legrand L, Monin ML, Ewenczyk C, Charles P, Komajda M, Brice A, Pandolfo M, Isnard R, Tezenas du Montcel S, Durr A.<em> JAMA Neurol.<\/em> 2015 Nov;72(11):1334-41.<\/li><li>Article : <a href=\"https:\/\/jamanetwork.com\/journals\/jamaneurology\/fullarticle\/2444310\" target=\"_blank\" rel=\"noopener\">A 22-Year Follow-up Study of Long-term Cardiac Outcome and Predictors of Survival in Friedreich Ataxia | Cardiology | JAMA Neurology | JAMA Network<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-1d7dafc elementor-widget elementor-widget-heading\" data-id=\"1d7dafc\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Syst\u00e8me nerveux<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-9b43dfb elementor-widget elementor-widget-text-editor\" data-id=\"9b43dfb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Caract\u00e9ristiques \u00e9volutives du Consortium Europ\u00e9en de l\u2019Ataxie de Friedreich pour les \u00e9tudes translationnelles (EFACTS): une \u00e9tude de cohorte de 3 ans.<\/strong> (2021)<ul><li>Reetz K, Dogan I, Hilgers RD, Giunti P, Parkinson MH, Mariotti C, Nanetti L, Durr A, Ewenczyk C, Boesch S, Nachbauer W, Klopstock T, Stendel C, Rodr\u00edguez de Rivera Garrido FJ, Rummey C, Sch\u00f6ls L, Hayer SN, Klockgether T, Giordano I, Didszun C, Rai M, Pandolfo M, Schulz JB;<em> Lancet Neurol.<\/em> 2021 May;20(5):362-372.<\/li><li>Article : <a href=\"https:\/\/www.thelancet.com\/journals\/laneur\/article\/PIIS1474-4422(21)00027-2\/fulltext\" target=\"_blank\" rel=\"noopener\">Progression characteristics of the European Friedreich&#8217;s Ataxia Consortium for Translational Studies (EFACTS): a 4-year cohort study &#8211; The Lancet Neurology<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-9d88ee8 elementor-widget elementor-widget-heading\" data-id=\"9d88ee8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Diab\u00e8te<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-5adafcc elementor-widget elementor-widget-text-editor\" data-id=\"5adafcc\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Le diab\u00e8te dans l\u2019Ataxie de Friedreich: \u00e9pid\u00e9miologies et prises en charges<\/strong> (2022)<ul><li>Tamaroff J, DeDio A, Wade K, Wells M, Park C, Leavens K, Rummey C, Kelly A, Lynch DR, McCormack SE. <em>Diabetes Res Clin Pract<\/em>. 2022 Apr;186:109828.<\/li><li>Article : <a href=\"https:\/\/www.diabetesresearchclinicalpractice.com\/article\/S0168-8227(22)00640-4\/fulltext\" target=\"_blank\" rel=\"noopener\">Friedreich\u2019s Ataxia related Diabetes: Epidemiology and management practices &#8211; Diabetes Research and Clinical Practice (diabetesresearchclinicalpractice.com)<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-fce1a9b elementor-widget elementor-widget-heading\" data-id=\"fce1a9b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Scoliose<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-49622c0 elementor-widget elementor-widget-text-editor\" data-id=\"49622c0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>La scoliose dans l\u2019Ataxie de Fridreich: caract\u00e9risation longiudinale d\u2019une large cohorte h\u00e9t\u00e9rog\u00e8ne<\/strong> (2021)<ul><li>Rummey C, Flynn JM, Corben LA, Delatycki MB, Wilmot G, Subramony SH, Bushara K, Duquette A, Gomez CM, Hoyle JC, Roxburgh R, Seeberger L, Yoon G, Mathews KD, Zesiewicz T, Perlman S, Lynch DR.. <em>Ann Clin Transl Neurol<\/em>. 2021 Jun;8(6):1239-1250.<\/li><li>Article : <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC8164850\/\" target=\"_blank\" rel=\"noopener\">Scoliosis in Friedreich&#8217;s ataxia: longitudinal characterization in a large heterogeneous cohort &#8211; PMC (nih.gov)<\/a><\/li><\/ul><\/li><li><strong>La scoliose des patients avec ataxie de Friedreich : r\u00e9sultats d\u2019une s\u00e9rie prospective cons\u00e9cutive.<\/strong> (2019)<ul><li>Simon AL, Meyblum J, Roche B, Vidal C, Mazda K, Husson I, Ilharreborde B. <em>Spine Deform<\/em>. 2019 Sep;7(5):812-821.<\/li><li>Article : <a href=\"https:\/\/www.sciencedirect.com\/science\/article\/abs\/pii\/S2212134X19300243?via%3Dihub\" target=\"_blank\" rel=\"noopener\">Scoliosis in Patients With Friedreich Ataxia: Results of a Consecutive Prospective Series &#8211; ScienceDirect<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-a48ae70 elementor-widget elementor-widget-heading\" data-id=\"a48ae70\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Troubles de la parole<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-53ef185 elementor-widget elementor-widget-text-editor\" data-id=\"53ef185\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Traitement pour les troubles de la parole dans l\u2019ataxie de Friedreich et autres ataxies h\u00e9r\u00e9ditaires<\/strong> (2014)<ul><li>Vogel AP, Folker J, Poole ML. <em>Cochrane Database Syst Rev.<\/em> 2014 Oct 28;(10):CD008953.<\/li><li>Article : <a href=\"https:\/\/www.cochranelibrary.com\/cdsr\/doi\/10.1002\/14651858.CD008953.pub2\/full\" target=\"_blank\" rel=\"noopener\">Treatment for speech disorder in Friedreich ataxia and other hereditary ataxia syndromes &#8211; Vogel, AP &#8211; 2014 | Cochrane Library<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-a95c971\" data-id=\"a95c971\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-90369ea elementor-widget elementor-widget-text-editor\" data-id=\"90369ea\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Documents associ\u00e9s<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-3de4628 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"3de4628\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-59be076 pdf2-colonne-laterale nouvelle-fenetre elementor-widget elementor-widget-text-editor\" data-id=\"59be076\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Retrouver la version PDF de la biographique propos\u00e9e ici<\/p><ul><li><a href=\"https:\/\/www.afaf.asso.fr\/wp-content\/uploads\/2023\/07\/AFAF-groupe-recherche-Revue-de-la-litterature-AF-juillet-2023.pdf\">AFAF groupe recherche &#8211; revue de la litt\u00e9rature d&#8217;articles scientifiques<\/a> &#8211; juillet 2023<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-7e1e4b3 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"7e1e4b3\" data-element_type=\"section\" data-e-type=\"section\" id=\"biologie\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-0de381f\" data-id=\"0de381f\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-096dc7e elementor-widget elementor-widget-heading\" data-id=\"096dc7e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Biologie fondamentale<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-0055359 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"0055359\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-inner-section elementor-element elementor-element-05ee210 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"05ee210\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-custom\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-171e9a3\" data-id=\"171e9a3\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9d71bc7 elementor-widget elementor-widget-heading\" data-id=\"9d71bc7\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">G\u00e9n\u00e9tique<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-b896cf8 elementor-widget elementor-widget-text-editor\" data-id=\"b896cf8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Ataxie de Friedreich : maladie autosomique r\u00e9cessive caus\u00e9e par une expansion r\u00e9p\u00e9t\u00e9e d&#8217;un triplet intronique GAA<\/strong> (1996)<ul><li>Campuzano V, Montermini L, Molt\u00f2 MD, Pianese L, Coss\u00e9e M, Cavalcanti F, Monros E, Rodius F, Duclos F, Monticelli A, Zara F, Ca\u00f1izares J, Koutnikova H, Bidichandani SI, Gellera C, Brice A, Trouillas P, De Michele G, Filla A, De Frutos R, Palau F, Patel PI, Di Donato S, Mandel JL, Cocozza S, Koenig M, Pandolfo M.. <em>Science<\/em>. 1996 Mar 8;271(5254):1423-7.<\/li><li>Article : <a href=\"https:\/\/www.science.org\/doi\/10.1126\/science.271.5254.1423?url_ver=Z39.88-2003&amp;rfr_id=ori:rid:crossref.org&amp;rfr_dat=cr_pub%20%200pubmed\" target=\"_blank\" rel=\"noopener\">Friedreich&#8217;s Ataxia: Autosomal Recessive Disease Caused by an Intronic GAA Triplet Repeat Expansion | Science<\/a><\/li><\/ul><\/li><li><strong>Le d\u00e9ficit en frataxine alt\u00e8re l&#8217;expression de g\u00e8nes dans des neurones IPSC et des cardiomyocites dans l&#8217;ataxie de Friedreich <\/strong> (2023)<ul><li>Angulo MB, Bertalovitz A, Argenziano MA, Yang J, Patel A, Zesiewicz T, McDonald TV.\u00a0<em>Mol Genet Genomic Med.<\/em>\u00a02023 Jan.<\/li><li>Article : <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC9834160\/\" target=\"_blank\" rel=\"noopener\">Frataxin deficiency alters gene expression in Friedreich ataxia derived IPSC\u2010neurons and cardiomyocytes &#8211; PMC (nih.gov)<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-7c8071a\" data-id=\"7c8071a\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-e57829a elementor-widget elementor-widget-text-editor\" data-id=\"e57829a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Documents associ\u00e9s<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-56fc1ef elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"56fc1ef\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-90d2a84 pdf2-colonne-laterale nouvelle-fenetre elementor-widget elementor-widget-text-editor\" data-id=\"90d2a84\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Retrouver la version PDF de la biographique propos\u00e9e ici<\/p><ul><li><a href=\"https:\/\/www.afaf.asso.fr\/wp-content\/uploads\/2023\/07\/AFAF-groupe-recherche-Revue-de-la-litterature-AF-juillet-2023.pdf\">AFAF groupe recherche &#8211; revue de la litt\u00e9rature d&#8217;articles scientifiques<\/a> &#8211; juillet 2023<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-244f4c7 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"244f4c7\" data-element_type=\"section\" data-e-type=\"section\" id=\"exam_paracliniques\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-117ef2c\" data-id=\"117ef2c\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-28c42ba elementor-widget elementor-widget-heading\" data-id=\"28c42ba\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Examens paracliniques<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-fdfda71 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"fdfda71\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-inner-section elementor-element elementor-element-a7946da elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"a7946da\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-custom\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-5db43f9\" data-id=\"5db43f9\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a125af7 elementor-widget elementor-widget-heading\" data-id=\"a125af7\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Imagerie<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-7c5f7f6 elementor-widget elementor-widget-text-editor\" data-id=\"7c5f7f6\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Structure c\u00e9r\u00e9brale et stades de la d\u00e9g\u00e9n\u00e9rescence dans l&#8217;ataxie de Friedreich : \u00e9tudes d&#8217;imagerie par r\u00e9sonance magn\u00e9tique du groupe de travail ENIGMA-Ataxia.<\/strong> (2021)<ul><li>Harding IH, Chopra S, Arrigoni F, Boesch S, Brunetti A, Cocozza S, Corben LA, Deistung A, Delatycki M, Diciotti S, Dogan I, Evangelisti S, Fran\u00e7a MC Jr, G\u00f6ricke SL, Georgiou-Karistianis N, Gramegna LL, Henry PG, Hernandez-Castillo CR, Hutter D, Jahanshad N, Joers JM, Lenglet C, Lodi R, Manners DN, Martinez ARM, Martinuzzi A, Marzi C, Mascalchi M, Nachbauer W, Pane C, Peruzzo D, Pisharady PK, Pontillo G, Reetz K, Rezende TJR, Romanzetti S, Sacc\u00e0 F, Scherfler C, Schulz JB, Stefani A, Testa C, Thomopoulos SI, Timmann D, Tirelli S, Tonon C, Vavla M, Egan GF, Thompson PM. <em>Ann Neurol<\/em>. 2021 Oct;90(4):570-583.<\/li><li>Article : <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC9292360\/\" target=\"_blank\" rel=\"noopener\">Brain Structure and Degeneration Staging in Friedreich Ataxia: Magnetic Resonance Imaging Volumetrics from the ENIGMA\u2010Ataxia Working Group &#8211; PMC (nih.gov)<\/a><\/li><\/ul><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-1674987\" data-id=\"1674987\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4e746e8 elementor-widget elementor-widget-text-editor\" data-id=\"4e746e8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Documents associ\u00e9s<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-f00bcce elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"f00bcce\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-5dd0324 pdf2-colonne-laterale nouvelle-fenetre elementor-widget elementor-widget-text-editor\" data-id=\"5dd0324\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Retrouver la version PDF de la biographique propos\u00e9e ici<\/p><ul><li><a href=\"https:\/\/www.afaf.asso.fr\/wp-content\/uploads\/2023\/07\/AFAF-groupe-recherche-Revue-de-la-litterature-AF-juillet-2023.pdf\">AFAF groupe recherche &#8211; revue de la litt\u00e9rature d&#8217;articles scientifiques<\/a> &#8211; juillet 2023<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-8b9661f elementor-section-full_width elementor-section-stretched elementor-section-height-default elementor-section-height-default\" data-id=\"8b9661f\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;stretch_section&quot;:&quot;section-stretched&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-40214b2\" data-id=\"40214b2\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d31c840 elementor-widget elementor-widget-shortcode\" data-id=\"d31c840\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"shortcode.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-shortcode\">\t\t<div data-elementor-type=\"wp-post\" data-elementor-id=\"578\" class=\"elementor elementor-578\" data-elementor-post-type=\"oceanwp_library\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-43c347e elementor-section-stretched elementor-section-content-middle elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"43c347e\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;stretch_section&quot;:&quot;section-stretched&quot;,&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-186798c\" data-id=\"186798c\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-04bb719 elementor-widget elementor-widget-image\" data-id=\"04bb719\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" src=\"https:\/\/www.afaf.asso.fr\/wp-content\/uploads\/elementor\/thumbs\/Logo-blanc_simple-1-q1ww1nh0svlc8x6kbcgbj84qq17mf0pfy8gdrayk1s.png\" title=\"Logo blanc_simple\" alt=\"logo AFAF (Association Fran\u00e7aise Ataxie Friedreich)\" loading=\"lazy\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-301d943\" data-id=\"301d943\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2b47be8 elementor-widget elementor-widget-text-editor\" data-id=\"2b47be8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Avancer ensemble,<\/p><p>C&#8217;est aussi pouvoir compter sur votre aide !<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-a663678 elementor-align-left elementor-mobile-align-left elementor-widget elementor-widget-button\" data-id=\"a663678\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-lg elementor-animation-grow\" href=\"https:\/\/www.afaf.asso.fr\/nous-soutenir\/donner\/\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">Je fais un don<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Cette page propose une veille bibliographique non exhaustive de la litt\u00e9rature scientifique en rapport avec l\u2019Ataxie de Friedreich, comprenant une s\u00e9lection&nbsp; d\u2019articles class\u00e9s par th\u00e9matique. 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